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Lenticonus

Lenticonus is a bulging of the lens capsule and the underlying cortex. The diagnosis of lenticonus is essentially a clinical diagnosis which is made by biomicroscopic examination. According to the localization of the conus a distinction is made between lenticonus anterior and lenticonus posterior. W Lenticonus consists of a bulge in the front of the lens (anterior lenticonus) (Figure 137-5) or at the back of the lens (posterior lenticonus) (Figure 137-6).Anterior lenticonus is associated with Alport syndrome. This multisystem disorder has three major findings: chronic nephritis, nerve deafness, and specific ocular abnormalities Anterior conical protrusion of the central lens surface caused by the thinning of affected anterior capsule. Deficiency of the subjacent epithelium resulting in irregular astigmatism. The lens defect may be an isolated finding or more commonly associated with Alport's syndrome. Alport's syndrome is an autosomal recessive disorder with chronic. Lenticonus is a rare congenital abnormality characterized by conical bulging of the posterior or anterior lens surface. If the bulging is global rather than conical, the condition is referred to as lentiglobus 1. Clinical presentation It produc.. Cataracts - Posterior Lenticonus. Liaison: Anngharaad Annie Reid. Email: annie.reid@cox.net. Posterior Lenticonus is an inherited, congenital lens abnormality which may result in cataract formation in both eyes. This type of cataract affects both male and female Samoyeds normally between 1 and 3 years of age

Involvement of the anterior lens capsule often results in bilateral anterior lenticonus (25%) and may be progressive. It is claimed that the severity of the lenticonus is a valuable marker in judging the overall disease severity. In early stages it may be difficult to detect but its presence is suggested by an 'oil droplet' reflex during. Definition of lenticonus in the Definitions.net dictionary. Meaning of lenticonus. What does lenticonus mean? Information and translations of lenticonus in the most comprehensive dictionary definitions resource on the web

Clinical Focus: The purpose of this value set is to represent concepts of a diagnosis for posterior lenticonus. Data Element Scope: This value set may use a model element related to Diagnosis. Inclusion Criteria: Includes concepts that represent a diagnosis of posterior lenticonus, including spherophakia. Exclusion Criteria: Excludes concepts that represent a diagnosis for 'unspecified eye. Dr. Allon Barsam shows how he performed cataract surgery in an 11-year-old patient with posterior lenticonus. He begins with trypan blue to visualize the anterior capsule. He then irrigates with a dispersive then cohesive viscoelastic to protect the endothelium in this young patient Posterior lenticonus is associated with progressive lens opacification. We report a series of 40 consecutive patients (41 eyes) with posterior lenticonus who were treated by three pediatric ophthalmologists between 1974 and 1988. Prior to cataract surgery, appropriate patients were treated with atro

Lenticonus - PubMe

Evaluation of anterior lenticonus in alport syndrome using tracey wavefront aberrometry and transmission electron microscopy. Kim KS, Kim MS, Kim JM, Choi CY Ophthalmic Surg Lasers Imaging 2010 May-Jun;41(3):330-6. doi: 10.3928/15428877-20100430-06 Lenticonus ceases to progress after cataract formation. Posterior lenticonus also occurs but is less common. Retina's injuries are localized in the inner limiting membrane/nerve fiber layer and may interfere with the homeostasis of retinal environment: nutrition of the overlying cells, removal of debris, and maintenance of the watertight. Lenticonus is a local bulging of the capsule of the crystalline lens and the underlying lens cortex. It commonly occurs at the anterior or posterior pole of the lens. Posterior lenticonus is a congenital defect which is limited to the eye and not associated with systemic diseases

Definition: Posterior lenticonus is a developmental anomaly of the lens in which the posterior portion of the lens bulges outward in a cone-shape. Incidence/Prevalence: Posterior lenticonus is much more common than anterior lenticonus. Sporadic and inherited cases have been described, particularly X-linked and autosomal dominant inheritance patterns Lenticonus is an uncommon condition where the crystalline lens cortex and the overlying capsule acquire a localized, cone-shaped deformation in one or both lens surfaces. Bilateral anterior lenticonus is commonly seen in Alport syndrome (AS), which is a hereditary (X- linked inheritance as the most common pattern) and progressive disease caused. Posterior lenticonus is one of the rar est anomalies of the human eye, but a somewhat similar defect at the front of the lens, anterior lenticonus, is rarer still. This latter defect is easily seen in the pupillary area, where tlie an terior lens contour is altered un til it may closely resemble a cone with a rounded tip

Lenticonus - an overview ScienceDirect Topic

Anterior Lenticonus Columbia Ophthalmolog

  1. lentiglobus: [ len″tĭ-glo´bus ] exaggerated curvature of the lens of the eye, producing an anterior spherical bulging
  2. Posterior lenticonus is a rare progressive disease characterized by protrusion of posterior lens capsule along with lens cortex into the vitreous cavity. Posterior lenticonus is more common but present unilaterally unlike anterior lenticonus, which presents bilaterally
  3. ation revealed bilateral anterior lenticonus. The patient underwent pre and post-operative corneal and anterior segment.
  4. Anterior lenticonus, which occurs in approximately 25% of patients with XLAS, is the pathognomonic feature of Alport syndrome. In this condition, the lens surface protrudes conically into the anterior chamber of the eye because of a thin and fragile basement membrane of the lens capsule. The lenticonus is most marked anteriorly because the.
  5. Although anterior lenticonus was observed as early as 1891, 2 Jaworski 3 was the first to describe the association of anterior lenticonus and nephropathies in 1910. In 1966, Arnott et al 4 reported anterior lenticonus as a specific sign of Alport syndrome
  6. About five years ago, a report of a typical posterior lenticonus which I had studied with the slit-lamp was published in the Archives of Ophthalmology,1 with an analysis of four similar reports, one by Vogt, two by Riedl and one by Whiting, all that had appeared at that time.2 Since then, through..
  7. LENTICONUS Wg CDR J.B. Singh Ahrr. Alport's Syndrome (1) which forms 25-- of all hereditary nephropathies consists of Glomerulonephritis sensorieneural deafness in about 60% of cases with or without ocular changes (2,3). Here we report a family of Alport's Syndrome whose two brothers first presented with anterior lenticonus in both eyes

Anterior lenticonus - This refers to a thinned-out central anterior capsule with or without anterior cortical opacities. Anterior lenticonus is said to be characteristic of Alport syndrome. Spontaneous rupture of the lens can occur, resulting in a hydrated total cataract Alport syndrome is a genetic condition characterized by kidney disease, hearing loss, and eye abnormalities. Most affected individuals experience progressive loss of kidney function, usually resulting in end-stage kidney disease. People with Alport syndrome also frequently develop sensorineural hearing loss in late childhood or early adolescence Alport syndrome is a genetic disorder affecting around 1 in 5,000-10,000 children, characterized by glomerulonephritis, end-stage kidney disease, and hearing loss. Alport syndrome can also affect the eyes, though the changes do not usually affect sight, except when changes to the lens occur in later life Posterior lenticonus is an uncommon abnormality in the shape of the crystalline lens, characterized by a spheroidal or conical protuberance affecting the posterior lens surface. It may be unilateral or bilateral. A male infant with bilateral posterior lenticonus is described, whose mother was found to have bilateral sutural cataracts Lenticonus (anterior) (posterior) (congenital) References in the ICD-10-CM Index to Diseases and Injuries. References in the ICD-10-CM Index to Diseases and Injuries applicable to the clinical term lenticonus (anterior) (posterior) (congenital) Lenticonus (anterior) (posterior) (congenital) - Q12.8 Other congenital lens malformation

An anterior lenticonus with a forward-protruding lens (shown) may occur in association with Alport syndrome, spina bifida, or Waardenburg syndrome. [1] Lenticonus is a rare congenital developmental abnormality in which the anterior or (more commonly) posterior lens surface projects spherically or conically due to thinning of the respective central lens surface posterior lenticonus. Search For A Disorder. Cataracts, Congenital, Autosomal Recessive 4. Clinical Characteristics. Ocular Features: This type of cataract has been reported in a single consanguineous family in which 4 sibs (2 males and 2 females) were diagnosed with cataracts shortly after birth

Lenticonus Radiology Reference Article Radiopaedia

The diagnosis of lenticonus is essentially clinical, which is made by biomicroscopic examination. According to the localization of the conus, a distinction is made between anterior and posterior lenticonus. Whereas AL is a part of the AS, posterior lenticonus is not usually associated with a systemic disease Clinical Focus: This value set contains concepts that represent a diagnosis of posterior lenticonus. Data Element Scope: This value set may use the Quality Data Model (QDM) category related to Diagnosis. Inclusion Criteria: Includes only relevant concepts associated with a diagnosis of posterior lenticonus, including spherophakia

Cataracts - Posterior Lenticonu

If the address matches an existing account you will receive an email with instructions to retrieve your usernam Posterior lenticonus or lentiglobus is a well-circumscribed, round or oval protuberance of the posterior lens capsule that is restricted to a 2.0 to 7.0 mm axial area [3 Gibbs ML, Jacobs M, Wilkie AO, Taylor D. Posterior lenticonus: clinical patterns and genetics J Pediatr Ophthalmol Strabismus 1993; 30(3): 171-5

Posterior lenticonus is a congenital anomaly of the lens characterized by a localized, round to oval, well-circumscribed protrusion of the posterior lens capsule and cortex [].Various theories. Posterior lenticonus is generally thought to occur as a sporadic condition. This study demonstrates that there is a family history of early-onset cataract in a significant number of bilateral. Posterior lenticonus is an infrequent congenital defect of the crystalline lens capsule, which produces a small conical projection on its posterior surface. The age of presentation is normally during the early childhood, and it is not associated with systemic illness

Alport syndrome is a genetic condition characterized by kidney disease, hearing loss, and eye abnormalities.People with Alport syndrome experience progressive loss of kidney function. Explore symptoms, inheritance, genetics of this condition Alport syndrome (AS) is a hereditary disease with various modes of inheritance, X-linked being the the most common. Anterior lenticonus is the characteristic abnormality along with perimacular and peripheral fleck retinopathy. Our two cases of AS had simultaneous anterior and posterior lenticonus with severe temporal macular thinning on optical coherence tomography with no specific renal. The manual capsulorhexis in patients with anterior lenticonus can be technically challenging due to increased fragility or elasticity of the lens capsule.3 Further, an atypical cogwheel-like tearing pattern during manual capsulorhexis could predispose to capsular runoff or rupture.6 FLACS obviates this difficulty by providing an automated, well. Anterior lenticonus - Occurs in approximately 25% of patients with XLAS; is the pathognomonic feature of Alport syndrome. Dot-and-fleck retinopathy - Most common ocular manifestation of patients with Alport syndrome, occurring in approximately 85% of males with XLAS

anterior lenticonus Hereditary Ocular Disease

  1. ology (8th Edition) Edit edition. Problem 2E from Chapter 18.4: Fill in the blanks.Lenticonus is conical protrusion of the _... Get solution
  2. ation during slit lamp exam. Bilateral cases associated with Alport Syndrome(Autosomal do
  3. Lenticonus is a cone-shaped deformation of the anterior or, more commonly, the posterior lens capsule. It may be inherited as an autosomal recessive trait or be associated with other abnormalities.
Pediatric posterior lenticonus cataract, posterior

Video: What does lenticonus mean

Lenticonus = conical protrusion. Lentiglobus = spherical protrusion. May be concurrent cataract, eg Miniature Schnauzer - with posterior lenticonus. Posterior lentiglobus is most commonly seen in association with multiple ocular anomalies including congenital cataracts Q12.8 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2021 edition of ICD-10-CM Q12.8 became effective on October 1, 2020. This is the American ICD-10-CM version of Q12.8 - other international versions of ICD-10 Q12.8 may differ. Applicable To Mainly posterior lenticonus, cataracts and microphthalmia were observed in the affected dogs, most of which were interrelated. Pathology was obtained from one of the cases demonstrating bilateral posterior lens capsule rupture with an unusual cellular reaction of the exposed lens material. Citing Literature Anterior lenticonus is an ocular abnormality that can occur in Alport's syndrome. In this study, Scheimpflug slit imaging analyses were employed for quantitative and objective evaluation of lens changes associated with Alport's syndrome Posterior lenticonus is associated with progressive lens opacification. We report a series of 40 consecutive patients (41 eyes) with posterior lenticonus who were treated by three pediatric ophthalmologists between 1974 and 1988. Prior to cataract surgery, appropriate patients were treated with atropine dilatation, spectacle correction.

Anterior lenticonus is considered a characteristic sign of Alport syndrome. Posterior lenticonus has been described as a rare manifestation in Alport syndrome and a review of the literature revealed a relative paucity of reports. We present here a case of Alport syndrome with anterior lenticonus and progressive posterior lenticonus Mainly posterior lenticonus, cataracts and microphthalmia were observed in the affected dogs, most of which were interrelated. Pathology was obtained from one of the cases demonstrating bilateral posterior lens capsule rupture with an unusual cellular reaction of the exposed lens material..

Anterior lenticonus is a characteristic ocular feature of Alport syndrome, leading to progressive vision deterioration. Surgical lens removal may be an option in such cases, and the role of femtosecond laser-assisted cataract surgery (FLACS) has been recently described Anterior lenticonus is a rare condition in which there is a conical or spherical protrusion ofthe anterior lens surface into the anterior chamber. At the present time some 42 cases have been reported (Table II), representing 30 per cent. ofthe total cases ofbothanterior andposterior lenticonus knownin the literature Lenticonus (/len·ti·co·nus/ (len″tĭ-ko´nus)) [lens + L. conus, cone] is a rare congenital anomaly of the eye characterized by a conical protrusion on the crystalline lens capsule and the underlying cortex

[Diagnosis: Posterior Lenticonus] eCQI Resource Cente

Eleven eyes of 6 patients with Alport syndrome had phacoemulsification with implantation of a single-piece acrylic hydrophobic intraocular lens (IOL) (AcrySof SA6OAT, Alcon) because of anterior lenticonus. All patients had excellent visual acuit Anterior lenticonus is a rare condition in which a por-tion of the crystalline lens capsule and underlying cor-tex bulge anteriorly. The conical protrusion results from a genetic defect in synthesis of type IV collagen, a major component of the lenticular basement mem Posterior lenticonus is a rare progressive disease characterized by protrusion of posterior lens capsule along with lens cortex into the vitreous cavity.... DOAJ is a community-curated online directory that indexes and provides access to high quality, open access, peer-reviewed journals Background and aims: Alport syndrome is an inherited disease with renal failure, and often a hearing loss, lenticonus and dot-and-fleck retinopathy. A retinal lozenge or dull macular reflex has been described in some patients. This study determined the prevalence and significance of this sign. Methods: Twenty-three patients from 14 families with X linked Alport syndrome and seven.

Alport syndrome is a genetic (inherited) disease. Signs and symptoms of Alport syndrome include hearing loss, eye problems, and blood in the urine, signifying loss of kidney function. Alport syndrome occurs in 1 out of 50,000 newborns. Mutations in the genes COL4A3, COL4A4, and COL4A5 cause Alport syndrome Systemic and ocular findings of Alport's Syndrome include: end stage renal disease, sensorineural deafness, anterior lenticonus and perimacular flecks. This case report describes a patient with classic Alport's Syndrome that was undiagnosed by various health care professionals until routine ophthalmic examination Posterior lenticonus--a bulging of the posterior capsule and cortex--is an acquired lens abnormality, which becomes increasingly opaque. We report an unusual case of bilateral posterior lenticonus.

Posterior lenticonus - a rare congenital anomaly of lens

Lenticular abnormalities

Management of Posterior Lenticonus - American Academy of

PurposeTo report the surgical treatment of 3 eyes of 2 patients with bilateral anterior lenticonus due to Alport syndrome using femtosecond laser-assisted cataract surgery (FLACS).MethodsTwo patien.. We report a case of intraocular lens (IOL) implantation with a continuous curvilinear capsulorhexis and phacoemulsification in a 30-year-old man manifesting anterior and posterior lenticonus. The surgery was uneventful and on follow-up, the IOL wa A patient with bilateral anterior lenticonus underwent successful bilateral phacoemulsification and implantation of a single-piece intraocular lens. Results The capsule tore in an atypical cogwheel-like tearing pattern during capsulorhexis Video Title: Lenticonus. Description: A video from Dr. Allon Barsam. Presenter/Interviewer: Dr, Osher introduces this video. Video Category: Video Journal of Cataract and Refractive Surgery Vol XXXII Issue 3, 2016. Keywords: Tags: lenticonus, Paediatric, White Catarac

Congenital defects of the lens

Management of posterior lenticonus - PubMe

Anterior lenticonus is an ocular abnormality that can occur in Alport's syndrome. In this study, Scheimpflug slit imaging analyses were employed for quantitative and objective evaluation of lens. Abnormal shape of the lens (anterior lenticonus), which can lead to a slow decline in vision as well as cataracts. Corneal erosion in which there is loss of the outer layer of the covering of the eyeball, leading to pain, itching, or redness of the eye, or blurred vision. Abnormal coloring of the retina, a condition called dot-and-fleck. Lenticonus. Cone-shaped lens due to bulging from a thin lens capsule; either anteriorly or posteriorly, rarely in both directions. Anterior. Usually males; bilateral; may be associated with Alport's syndrome (see Congenital Cataract section below). Figure 8-2 Anterior lenticonus in a patient with Alport's syndrome Alport syndrome is a rare basement membrane disorder that may include ocular manifestations: dot-and-fleck retinopathy, anterior lenticonus, posterior polymorphous corneal dystrophy, or temporal macular thinning. It is primarily an X-linked inheritance condition (85%)

Exam 1 at Southern College of Optometry - StudyBluePosterior Lenticonus - TCorneal dystrophy, epithelial basementPosterior Polymorphous Corneal Dystrophy (PPMD)Evaluation of Lenticular Irregular Astigmatism Using

The dog with lenticonus has a conical protrusion of his eye's lens; if he has lentiglobus, the bump is spherical. The condition often occurs with other conditions, such as congenital cataracts and retinal dysplasia. This condition can affect a dog's visual acuity, but treatment is not usually necessary The code Q12.8 is valid during the fiscal year 2021 from October 01, 2020 through September 30, 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q12.8 might also be used to specify conditions or terms like anterior lenticonus, anterior lentiglobus, congenital anterior capsular pigmentation, congenital pigmentation of. A cataract is any light scattering opacity of the lens. It is estimated that congenital cataracts are responsible for 5% to 20% of blindness in children worldwide. Incidence varies from country to country. One retrospective study of the prevalence of infantile cataracts in the U.S. showed a rate of 3-4 visually significant cataracts per 10,000 live births.[1] This is a similar rate to. Alport syndrome is an inherited disease of the glomerular basement membrane caused by abnormalities in type IV collagen. Gubler MC. Inherited diseases of the glomerular basement membrane Alport's syndrome is an inherited disease of the glomerular basement membrane caused by abnormalities in type IV collagen. Gubler MC. Inherited diseases of the glomerular basement membrane